Single-stage open repair of severe asymmetric pectus excavatum and mitral valve replacement in connective tissue disease

Pau, Cheong Ping and Chong, Kee Soon and Yakub, Mohd Azhari and Abdul Khalil, Alizan (2022) Single-stage open repair of severe asymmetric pectus excavatum and mitral valve replacement in connective tissue disease. Asian Cardiovascular and Thoracic Annals, 30 (4). 480 – 482. ISSN 0218-4923, DOI https://doi.org/10.1177/02184923211014004.

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Abstract

We present a 14-year-old boy with Loey–Dietz syndrome with severe mitral regurgitation, pectus excavatum and scoliosis. The Haller index was 25. The heart was displaced into the left hemithorax. The right inferior pulmonary vein was very close to the sternum and vertebral body. Single-stage surgery was performed. An osseo-myo-cutaneous pedicled flap was created by sterno-manubrial junction dislocation and rib resection with bilateral internal mammary arteries supplying the flap. Cardiopulmonary bypass and mitral valve replacement was performed. The defect was bridged with three straight plates. The flap was laid on top and anchored. Early outcome at three months was good. © The Author(s) 2021.

Item Type: Article
Funders: None
Uncontrolled Keywords: Adolescent; Connective tissue diseases; Funnel chest; Humans; Male; Mitral valve; Sternum; Treatment outcome; Celecoxib; Fentanyl; Paracetamol; Tramadol; Adolescent; Analgesia; Article; Bleeding; Cardiopulmonary bypass; Case report; Clinical article; Computer assisted tomography; Connective tissue disease; Echocardiography; Funnel chest;Human; Intensive care unit; Loeys dietz syndrome; Lung function; Male; Mitral valve regurgitation; Mitral valve replacement; Myocutaneous flap; Noninvasive ventilation; Operation duration; Osteotomy; Outcome assessment; Pedicled skin flap; Preoperative period; Respiratory failure; Single stage open repair; Skin incision; Thorax wall reconstruction; Complication; Connective tissue disease; Diagnostic imaging; Mitral valve; Sternum; Treatment outcome
Subjects: R Medicine > RD Surgery
Divisions: Faculty of Medicine > Surgery Department
Depositing User: Ms. Juhaida Abd Rahim
Date Deposited: 23 Oct 2023 03:59
Last Modified: 23 Oct 2023 03:59
URI: http://eprints.um.edu.my/id/eprint/43504

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